Huntington’s disease is also known as Huntington’s Chorea. It is inherited neurodegenerative disorder which impaired behavioural and cognitive function. There is also a lack of coordination and unsteady gait. Chorea is the most common and hyperkinetic, hyperactivity movement disorder with the involvement of upper limb, lower limb, face and trunk. Untreatable, Progressive Chorea condition further known as Huntington’s disease. It can be defined as involuntary, explosive, and jerking movement of bodily activities. These activities looks like a dancing movement. Common cause of this disorder is know to be inheritance. Other causes include complications during labour and premature birth. As per Ayurvedic literature Huntington’s disease can be understood with the reference of ‘Tandav Rog’ or ‘Tandav vata’. Tandava means ‘Nrityam' dancing with violent gesture like Lord Shiva. There is an involvement of Vata dosha in Tandava Rog explained by Acharya. Purpose: The case study focuses on the management of patient with Ayurvedic approach. Materials and Methods: A Single case study. In this case study a male patient came to OPD and was diagnosed for Tandava Vata. He was given management like Shirobasti, Sarvanga Abhyanga, Sarvanga Shashtika Shali Pinda Swedana and Basti for 28 days along with some oral medications. The patient showed marked improvement in his symptoms. Qualitative data was obtained from the inpatient department of Kaumarbhritya, Government Ayurved Hospital, Nagpur. Subject was assesed on the basis of developmental milestone such as fine motor, Gross motor, social skills and communication skills. Other parameters also checked such as investigations, Present history, past history and family history. Various types of Ayurvedic treatment modalities have been given to the subject such as panchakarma and internal medications. Result and Conclusion: The subjects have shown remarkable improvements in the sign and symptoms within one month of treatment. Ayurvedic therapeutic procedures are very well made use in the management of Tandava Rog. There is some evidence on the beneficial effect of Ayurvedic treatment on Chorea as shown in our case. Therefore, ayurvedic approach should be considered as a treatment option in patients with severe chorea that is Tandava Rog.