Background: Hughes-Stovin Syndrome (HSS) is a rare clinical entity comprised of thrombophlebitis, multiple pulmonary and/or bronchial aneurysms. Medical literature has documented fewer than 40 cases of HSS. Its pathogenesis and etiology are still unknown. It is considered as a variant of Behcet’s disease (BD). HSS is being managed either medically or surgically.
Case Presentation: We report the case of a 32-year-old Saudi male patient with Hughes-Stovin syndrome who initially presented with a pulmonary embolism. Later, he developed hemoptysis that was treated successfully with methylprednisolone. The genetic, etiologic, and pathologic basis of HSS should be explored more in the future to clearly elucidate the disease.
Conclusion: Exploration of better and optimal medical and surgical therapeutic regimens is a need for time to treat and prevent morbidity in BD and HSS. There is a dilemma of anticoagulation in these patients that needs to be addressed and investigated properly.
